Abstract

The Sialoblastoma is a rare malignant tumor of the epithelial cells of the salivary glands, with less than 100 cases reported. Its main location is in the parotid gland, but it may affect other salivary glands. The diagnose should be investigated in cases of a congenital tumor in the topography of these salivary glands and may be confirmed by open biopsy, or after complete excision. Due to rarity of the disease, there is no consensus for the conduct in the literature, but surgical treatment shown better outcomes. The adjuvant treatment with chemotherapy may be feasible to advanced metastatic cases.