Introduction
Double orifice mitral valve (DOMV) is a rare cardiac anomaly. It is
uncommon to find it as an isolated lesion and is seen associated with
atrioventricular septal defects (AVCD) in approximately 5% of
cases.1 Although a number of case reports of DOMV have
been reported2-4, literature highlighting its surgical
management is scarce. The challenge lies in, repair of DOMV associated
with regurgitation, without producing new stenosis, as inherent nature
of this valve predispose it to stenosis. We describe a case report of
DOMV associated with AVCD, which was detected incidentally
intraoperatively in a 2 year male child with severe mitral regurgitation
(MR) and was managed successfully.