Legends:
Fig 1.
Coronal (A) T2-weighted MRI of the abdomen show a huge retroperitoneal mass with partially well delineated margins and markedly heterogenous intensity signal, causing upper displacement of the right kidney and enlarging of neual foramina. Multiple subcutaneous, paraspinal and pelvic plexiform neurofibromas with the characteristic target sign are shown. Axial MRI demostrate a mostly homogeneous isointense retroperitoneal mass in T1- weighted image (B) with peripheral inhomogenous contrast enhancement after gadolinum intravenous administration (C) and heterogenous diffusion restriction in diffusion- weighted MRI (D) and ADC map (E).