Figures
Figure 1. Frontal and lateral radiography of the femur shows
bilateral symmetric distal metadiaphyseal cortical thickening and
diffuse medullary sclerosis with loss of corticomedullary
differentiation.
Figure 2A-E. Fibrocollagenous stroma with clusters of foamy
histiocytes (A); thickened bony trabeculae with features of cementum
surrounding intertrabecular space filled with fibrous stroma (B) with
variable proportion of foamy histiocytes (C). There is also infiltration
of the foamy histiocytes accompanied by scattered lymphocytes within the
soft tissue (adipose tissue at the right top corner) and rare
multinucleated cells (arrow and inset) (D). Thickened trabeculae of
laminar bone and its character under polarized light (inset) (E).
Figure 3A-C. Axial pre-contrast (A) and post-contrast (B) chest
CT shows soft-tissue encasement of the aortic arch and descending
thoracic aorta (coated aorta sign). On lung window (C) there are
randomly distributed multiple different sized lung cysts with right
lower lung ground glass opacities.
Figure 4A-D. Axial (A and B) contrast enhanced CT of abdomen
shows ill-defined, plaque-like, heterogeneous soft tissue lesion
infiltrating bilateral peri-renal spaces with thickening of anterior and
posterior renal fascia ( hairy kidney sign) and no sign of
hydronephrosis is seen. On the same images there is fat stranding of the
mesentery. Coronal view (C and D) shows mild soft tissue encasement of
the abdominal aorta and the proximal bilateral common iliac arteries
(Coated aorta sign).