Introduction:
Malignant spindle cell tumors account for 1% of the total head and neck
cancers and of all 5-10% are classified as sarcomas in adult population
[1]. According to World Health Organization (WHO) classification in
2017, the head and neck sarcomas are divided into eight histological
subtypes: undifferentiated pleomorphic sarcoma, fibrosarcoma,
angiosarcoma and malignant peripheral nerve sheath tumor (MPNST)
[1]. Due to diverse histopathology variants, the diagnosis of head
and neck sarcomas poses significant challenges towards diagnosis and
management. Sinonasal sarcoma is one of the unique tumor now presented
by WHO and has been added in the classification of head and neck
malignancies recently [2].
Herein we are reporting a rare case of sinonasal sarcoma in 38-years old
female presented to department of otolaryngology and head and neck
surgery, Benazir Bhutto Hospital, Rawalpindi.