FIGURE LEGENDS
Figure 1: (a) The four-chamber view revealed concordant atrioventricular
and ventriculoarterial connections and intact ventricular septum. The
right heart was significantly dilated. (b) Color flow mapping
demonstrated severe tricuspid regurgitation. (c) The short axis view of
the great arteries revealed a rudimentary pulmonary valve with severe
regurgitation of its orifice, and the pulmonary branches were not
dilated. (d) The pulsed-wave Doppler demonstrated the to-and-fro blood
across the dysplastic pulmonary valve (PG at 75 mmHg and peak velocity
at 432 cm/s). LV: left ventricle; RA: right atrium; RV: right ventricle;
TV: tricuspid valve; PA: pulmonary artery; PG: pressure gradient.
Figure 2: The arrow marked the delimitation between the normal cardiac
muscle and proliferative fibrous tissue. This area demonstrates absent
pulmonary valve leaflets which is substituted with a restrictive ring of
thickened tissue.