FIGURE LEGENDS
Figure 1: (a) The four-chamber view revealed concordant atrioventricular and ventriculoarterial connections and intact ventricular septum. The right heart was significantly dilated. (b) Color flow mapping demonstrated severe tricuspid regurgitation. (c) The short axis view of the great arteries revealed a rudimentary pulmonary valve with severe regurgitation of its orifice, and the pulmonary branches were not dilated. (d) The pulsed-wave Doppler demonstrated the to-and-fro blood across the dysplastic pulmonary valve (PG at 75 mmHg and peak velocity at 432 cm/s). LV: left ventricle; RA: right atrium; RV: right ventricle; TV: tricuspid valve; PA: pulmonary artery; PG: pressure gradient.
Figure 2: The arrow marked the delimitation between the normal cardiac muscle and proliferative fibrous tissue. This area demonstrates absent pulmonary valve leaflets which is substituted with a restrictive ring of thickened tissue.